Interactive Transcript
0:01
So let's wrap up.
0:02
So we have our four choices for differential diagnosis
0:06
for diffuse cystic lung disease at most centers.
0:09
And so remember lamb, we're talking about thin walled,
0:12
pretty cyst, diffuse distribution round
0:14
and oval intervening.
0:15
Lung should be normal. Remember lamb can be either related
0:20
to tube sclerosis
0:22
or it can come, um, without
0:24
that underlying disease abnormality.
0:27
And so in both these cases, you're gonna look for angio,
0:29
my lipomas in the upper abdomen.
0:30
Even in patients who have isolated lam
0:33
and not TS related lam,
0:34
they can still get angio myel lipomas.
0:37
Every once in a while you're gonna see some scattered subs,
0:40
solid nodules throughout the lungs, usually subs solid,
0:42
very small and often oftentimes innumerable.
0:46
And so in the setting of lamb, you should be thinking,
0:48
especially TS lamb.
0:49
You should be thinking about multifocal micro nodular
0:51
pneumococci hyperplasia.
0:53
Some people would just call it pneumococci hyperplasia,
0:55
but we can see those as well.
0:57
Uh, probably worth following them at least a little bit
0:59
to make sure that there's no adenocarcinoma in any
1:02
of these more dominant nodules.
1:05
TLCH, we talked about that.
1:06
It's just completely different from the other, uh,
1:07
diffuse cystic lung disease.
1:09
So the cytal walls can be thin
1:11
or thick, they're ugly, they're upper lung preponderant.
1:14
They spare the schizophrenic angles can be oftentimes
1:17
bizarre shaped, very, very different.
1:19
And heterogeneous, remember
1:21
that they emanate from those central lo nodules.
1:24
And you should be looking
1:25
for these cheerios like small cavitary
1:27
nodules and an end stage.
1:28
They can give you this burnt out appearance,
1:30
that complex pattern of some upper lung preponderant,
1:33
fibrosis, emphysema, diffuse cystic lung disease,
1:37
and sometimes some scattered central lobular nodules.
1:40
So pretty specific for P-P-L-C-H.
1:42
Again, if there's that relative basal sparing in somewhat
1:46
strong smoking related history, LIP.
1:49
In adults, we're gonna see that most common Sjogren's
1:51
syndrome and sometimes even deficiencies.
1:53
These are basar predominant cyst. They're pretty cysts.
1:56
Look for peron ster and subpleural cyst.
1:58
Um, every once in a while you're gonna see some concomitant
2:01
inflammation, but in my
2:02
clinical practice, that's not that common.
2:04
LIP and bird hug debate look very similar.
2:06
Bird Hug Bay also gives you thin walled cyst.
2:08
But remember, look for those renal tumors.
2:10
So bird hug debase syndrome also predispose you
2:13
to renal tumors, renal cell carcinomas and oncocytoma.
2:17
And then for bird hug debase syndrome.
2:20
The per mediastinals are quite characteristic.
2:23
Thank you very much. I.