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Lymphangioleiomyomatosis (LAM)

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0:00

So now let's move on to lamb or lymphangitis.

0:03

My mitosis, I will probably just call it

0:05

lamb because that's a mouthful.

0:07

And so the cysts here are quite different from the cysts

0:09

that we saw in long Han cell histiocytosis.

0:12

And so these cysts are pretty cysts, beautiful cysts,

0:16

thin walled, uniformly thick, thin walled intervening.

0:18

Lung is almost always normal.

0:20

They're usually round and oval shape as like this,

0:24

but they're, they're pretty, they're diffusing their

0:27

distribution both in the axial and the zonal plane.

0:30

And so they will involve the caa, phrenic socy.

0:33

Sometimes you could see a little bit of a basler gradient,

0:36

but not always, for me at least clinically,

0:39

I think maybe two thirds,

0:41

three quarters have a diffuse distribution

0:43

and a small minority.

0:44

But a substantial minority will have a little bit

0:46

of base or predominance.

0:47

But these just look different.

0:49

And usually these cases of lymphangitis mitosis,

0:51

there are a lot of these pretty nodules, these

0:55

patients in the upper abdomen.

0:57

Not uncommon to see renal angio, my lipomas.

1:01

So these tumors with areas of fatty abnormality as well.

1:04

Fatty attenuation, classic renal, anti my lipomas.

1:07

Sometimes you can see them in the, the liver as well,

1:11

or frank lipomas.

1:13

Also, remember these are both minutes,

1:15

so minimum intensity projection images

1:17

in any diffuse cystic lung disease.

1:19

But particularly if you have more cysts like in lymphangitis

1:22

mitosis, you tend to see more, more cyst in terms of, uh,

1:25

profusion throughout the lungs.

1:27

And so when you see that degree

1:29

of diffuse cystic lung disease,

1:30

this pushed the patient at risk for a pneumothorax.

1:34

This patient popped a pneumo here in the right hemothorax,

1:38

as you can see.

Report

Faculty

Jonathan H. Chung, MD

Professor of Radiology and Division Chief of Cardiothoracic Imaging

UCSD - University of California San Diego

Tags

Neoplastic

Lungs

Chest CT

Chest

CT