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Case: Ebstein’s Anomaly

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So this was an 11 day old infant who was transferred

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to our institution from an outside hospital with, um,

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concern for respiratory distress.

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This patient, he, uh, came here to be imaged

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with echocardiography.

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Um, this is the, uh, uh, frontal portable view

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of the chest demonstrating a markedly enlarged

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cardiac silhouette.

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Um, this patient has an inferior approach, uh,

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peripherally inserted central catheter.

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So a pick. This is an enteric tube,

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which is a little on the high side.

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This tip, I would love for it to be extending into the,

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uh, gastric body.

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Here's at the inferior aspect of the GE junction probably,

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and then there's this, uh, little peripheral

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IV in the left anti cubital fossa as well.

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But, uh, we already talked about the primary abnormality in

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this infant, and that is this basically wall to wall heart.

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This heart is so enlarged that it nearly, um,

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nearly occupies the entirety of the transverse diameter

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of this thoracic cavity.

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Um, so the good news is we don't have to make the diagnosis

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of Epstein anomaly, uh, just based on this chest x-ray.

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Our job is to say that it's an abnormal cardiac morphology,

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and then the patient will go on to echocardiography,

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to definitively diagnose the, um, the cardiac structures,

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as well as get an idea of the function of this, um, patient.

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The other thing we should be on the lookout

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for is any complications of congestive heart failure.

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So, um, uh, pulmonary edema, uh, uh, plethora,

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pulmonary vasculature, et cetera.

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But in this patient, um,

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all we have is the marked cardiomegaly.

Report

Text

Faculty

Judy H. Squires, MD

Associate Professor of Radiology

UPMC Children's Hospital of Pittsburgh

Tags

X-Ray (Plain Films)

Pediatrics

Neonatal

Congenital

Chest

Cardiac Chambers

Cardiac