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Cases: Bronchopulmonary Sequestration (BPS), Postnatal Diagnosis

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The remaining cases that we'll discuss

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of bronchopulmonary sequestration are different than the

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first three and that these were not diagnosed prenatally.

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Here I am showing you a chest radiograph of a young child

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who came to the emergency department for cough.

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It was noted at the time of interpretation

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that there is this confluent retro cardiac opacity

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and we can see on the lateral view more subtly

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that it's hiding back in here somewhere.

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And so given the patient's symptoms, the radiologist thought

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that this was most likely going to be a pneumonia

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and it is quite a typical look for pneumonia as well.

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However, due to some clinical concerns, the patient went on

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to get a CT scan.

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And so we have here

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an axial contrast enhanced ct

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and this CT was actually

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of the abdomen due to clinical concerns.

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But we can see the lower chest

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and that there is a subtle rounded structure

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that seems a little bit separate from the pleural

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fluid adjacent to it.

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This corresponds with

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that confluent opacity seen on the radiographs.

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Because of this more focal appearance here,

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this patient went on to have an MRI.

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And so we have 3M RI

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images, axial images.

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The first one I'm showing here is the T two

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fat SAT images and then we have T one fat SAT images without

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IV contrast and then T one fat sat images with IV contrast.

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Focusing on the T two we can see that same rounded structure

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that's hypo intense on the T two

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with some surrounding pleural fluid.

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There's also some pleural fluid on the other side

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and there's also some adjacent atelectasis on both sides.

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But the main finding here is this hypo intense lesion

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on T one images.

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It's an intermediate intensity surrounded

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by pleural fluid again.

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And then on T one post contrast images, we can see

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that there is no internal enhancement of the lesion.

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There is enhancement of adjacent atelectatic lung,

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so this turned out

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to be an extra low bar bronchopulmonary sequestration

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that had tourist

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and when it tourist its blood supply was cut off

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and hence there's no enhancement of the lesion.

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And so this is an unusual

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but possible complication of extra low bar sequestration.

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This one happens to be intrathoracic

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and this patient went on to surgery and had it resected

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and it was proven at pathology

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to be a tourist extra lobar sequestration.

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This next case is of a baby who originally had radiographs,

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which I'm not showing here, and also had an ultrasound.

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The ultrasound showed

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What looked like a supra renal mass

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and so they went on to have a CT scan.

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Here we have contrast enhanced

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angiographic images in axial and coronal plane

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and I'll start with the coronal plane.

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You can see here nice opacification

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of the aorta in the abdomen.

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We can see the left kidney here

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and the right kidney here and superior.

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And separate from the left kidney is this

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ill-defined lobular mass.

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That would be easy to ignore if you weren't paying

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attention, but it is not

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a normal structure is not a normal adrenal gland.

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And as we scroll, you'll note

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that there are some prominent vessels centrally

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that you can trace back to a systemic branch

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of the aorta.

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So this has a feeding artery coming off

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of the systemic arterial supply going into this

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non-specific lobular soft tissue mass.

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But because we saw that large feeding artery,

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the top differential here was an extra low bar

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intraabdominal broncho pulmonary sequestration,

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which this was proven to be at pathology.

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I'm not showing the original ultrasound here,

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but interestingly the normal adrenal gland was actually

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found separately, which can be quite hard to do,

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but it was found separately so it was not an adrenal mass.

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The final case I will show is of an older child

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who started out with a radiograph

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and they came in for acute respiratory symptoms

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and somewhat similarly to our first case,

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we see a confluent retro cardiac opacity causing

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silhouetting of the diaphragm.

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We don't see the diaphragmatic margin very well

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and so this was thought to be pneumonia at the time

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of this interpretation.

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The patient was treated and their symptoms resolved,

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but then two years later they came back

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and had a subsequent radiograph.

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Here we have both frontal and lateral views

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and we have a very similar picture.

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So two years later, very similar confluent retro cardiac

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opacity causing silhouetting

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of the diaphragm all the way out here.

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And we can see it's harder

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to find its borders on the lateral,

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but note the absence of the second diaphragmatic margin

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so we can see the right diaphragm clear as day,

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but you can't see the left diaphragm.

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And the reason is it's silhouette out by this thing here.

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So because of this, this patient went on to have a CT scan

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and we have tri plaine images

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and the axial have both soft tissue and lung windows.

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So we'll focus on the soft tissue window axials first.

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We can see in that left lower lung, many cystic

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foci all clustered together

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with some enhancing intervening sector.

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And importantly, although we do not see an obvious

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feeding artery coming directly from the aorta,

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and we do see some vessels that seem to be communicating

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with the pulmonary arteries in this case a pathology.

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This also turned out to be a sequestration.

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This was an intra lobar sequestration that was still cystic

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and we can see on the lung windows,

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but it's causing perhaps a little bit of ectasis.

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And on the additional planes,

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I'm gonna change the lung windows a little bit.

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We can get a sense of its size

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and relationship to the mediastinal structures.

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And again, despite not being able

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to see an obvious systemic feeding artery a pathology,

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this was a broco pulmonary sequestration.

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Just another look. So you can see the variety of appearances

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that this type of lesion can have.

Report

Faculty

Grace S Mitchell, MD, MBA

Pediatric Radiologist

Children's Mercy Hospital Kansas City

Tags

X-Ray (Plain Films)

Pediatrics

Neonatal

MRI

Lungs

Congenital

Chest

CT