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Angiomyolypoma

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0:01

So here we have a 56 year old woman with a history of hypertension and

0:04

gastroesophageal reflux disease. She's referred.

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In the outpatient Surgery Clinic as part

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of a preoperative consultation for

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ventral hernia repair.

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She reports no symptoms beyond the modern discomfort that

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she is felt due to what she feels

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is an abdominal bulge physical examination is

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performed and reveals a reducible hernia, because otherwise within

0:28

normal limits the vitals for this patient are

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notable for a blood pressure of 143 over 92.

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Top normal or slightly elevated rather. She's

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referred for a preoperative CT scan as

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part of a surgical planning.

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So in the reading room, what do we see?

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So what's the impression here? We have an anterior abdominal

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wall. Hernia particularly large which we would have seen before.

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Containing transverse colon with extensive herniation against

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partly see it here, but no signs of

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strangulation.

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However, very carefully imaged here.

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We have the right adrenal gland

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which is thought to be displaced Superior immediately.

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and Inseparable from

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this Mass which is hypodens not

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enhancing in nature measuring about 12

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by 9.5 by 10.6 centimeters. So this

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low density hypodens non-enhancing mass

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occupying the Retro peritoneal space.

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It doesn't seem to have any signs of liver or kidney invasion.

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There are some fine septations if we had to clean a

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little bit more.

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Into this lesion it suggestive of mesenteric

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fat within the mass.

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The patient scheduled for CT guided biopsy of her right

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adrenal mass. And here we see the needle

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Progressively being Advanced and the CT guidance CT

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fluoroscopy. In this case into the masking question the

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IR performs an uncomplicated biopsy technically

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successful. The tissue sample is

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stored in formula and sent to the Pathology Department for analysis.

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The path report comes back thin fragment

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of adipose tissue with admix Desmond stain

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cells concerning for an angiomyolipoma, which

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as we know is a tumor of and you must

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thinkable myomuscular and lipoma fatty

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elements.

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This for all intense purposes is benign tumor. So although

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there was a limited amount of tissue. The thought

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is that additional sampling was actually

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required for definitive classification.

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So the patients referred for general surgery consultation.

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The surgeon is actually concerned for sarcominous Mass.

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The patient is scheduled for Ratchet pensional tumor resection

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on block adrenalectomy with concomitant

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repair of eventual. Hernia.

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Her surgical course is particularly uncomplicated thankfully

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and she is discharged from the hospital the day after

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her operation.

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So what is a surgical pathology report read what we

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see here is the Retro bedroom Mass contains ample

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fatty tissue with intermix Desmond

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staining cells again consistent with

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Andrew. Myelypuma a benign tumor.

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So the adjacent adrenal tissue also unremarkable no

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evidence of malignant features.

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In retrospect friends was open

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surgery necessary to diagnose his patients regular Mass.

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Yes. This was a suspicious mass

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that needed direct sampling or no

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radiographic features of this

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Mass suggested that's benign C.

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If you said no radiographic features

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of this Mass suggested, it's been dignity. Then you

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would have been spot on per the American College

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of radiology criteria the diagnosis of

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angiomyelopoma may be made radiator graphically.

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This is a mass with gross fat

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and it's particularly important for us

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to be aware of that in the setting.

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So per the ACR criteria, which features of

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this Mass suggested Angie my life homo.

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Is it the size greater than 5 centimeters?

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Is it the shape?

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Is it the presence of microscopic fat?

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Or is it the attenuation pattern?

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Well, if you heard me letting the cat of the

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bag, the presence of ractoscopic fat should have told

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this perspectively that this in the

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setting of a non calcified solid renal

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Mass indicates a benign angiomyelopoma

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with virtual certainty.

Report

Faculty

Mikhail CSS Higgins, MD, MPH

Director, Radiology Medical Student Clerkships; Director, ESIR

Boston University Medical Center

Tags

Retroperitoneum

Peritoneum/Mesentery

Oncologic Imaging

MRI

Interventional

Genitourinary (GU)

Gastrointestinal (GI)

CT

Body