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Bicuspid Aortic Valve

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In this next video, I wanna discuss bicuspid valves.

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So it turns out for bicuspid valves in tavr, these patients, um,

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have similar long-term outcomes to patients with the normal tricuspid

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valve. However, they do have a higher rate of paravalvular regurgitation. Um,

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and so for that reason, we really wanna know, uh,

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about these patients who have bicuspid valves ahead of time. And if we see it,

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we should certainly report it, um, to the interventionalists. Uh,

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on the right hand side, this figure you see, um,

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this is actually telling us about the rate of, um,

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paravalvular leak in patients with. Um,

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it's divided up into early and next gen devices. Um,

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but basically you see that for both the early devices and the more recent

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devices, the rate of paravalvular leak is always higher with patients with, uh,

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bicuspid aortic valve compared to those with a tricuspid, uh, aortic valve.

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So for that reason, it's important we, uh, reported.

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And also it's important to give some information about the type of bicuspid

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aortic valve. And there's really two major types, um,

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that you're gonna run into. This is a really nice review that came out, uh,

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back in 2021.

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It's a consensus statement on nomenclature and classifications of bicuspid

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aortic valves. And it turns out, you know, if, if you look into this, there,

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there are all sorts of different systems that have been developed for describing

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the aortic valves. Um,

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and different ones are used by different people and they're a little bit

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confusing with a lot of overlap. So this was a really nice paper that came out,

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uh,

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to basically come up with a consensus among imagers for how to describe these,

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um, aortic valves. And it's been approved by all the various big societies.

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Um, so what they came up with was that there are three major types of subgroups.

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Um,

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the largest 99 to 95% of patients being the fused by cuspid aortic

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valve. And those cases, um,

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they can actually be a little bit confusing because if you look at 'em,

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you'll see three aortic sinuses and cupps. However,

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two of them are stuck together and a lot of times they'll have what's called a

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RAF or a ridge between the two. Um, and that ridge, um,

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is often thickened and calcified in in most of these patients.

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The confusing part of this is if you're looking in diastole when the valve isn't

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open, you'll see three cusps, you'll see the RA or the ridge,

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which makes it look like there may be two separate cusp there.

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And you might not even realize that you're dealing with a bicuspid valve until

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you see the opening when it opens.

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It should have that same typical fish mouth opening that you see with any type

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of bicuspid valve because of the fusion of those, those two cusps.

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Now the other one which is less common is the two sinus bicuspid aortic valve.

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And this is actually the one that we think of traditionally as like,

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this is our sort of mental picture, at least for me, of what an aortic valve,

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a bicuspid aric valve looks like.

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And that's where you have only two sinuses and two cusps. And you know,

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it's obviously very obvious to figure out when you see these valves.

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And then the last category, which has a little question mark here because it

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Hasn't been well studied,

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is when you basically have incomplete fusion of two over the cusps and they call

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it partial fusion b a V. Um,

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the thought here is that this may be some sort of degenerative process where

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there have been some calcification and thickening of the leaflets that that lead

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to some partial fusion. So it's not completely a bi spiric valve,

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but somewhere in between. So just here some figures to show you this.

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Um, and this is actually referring back to that, um, guideline from, uh,

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J C C T A guideline on tavr, um, CT reporting. Um,

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and this guideline actually tells us a little bit about some of the other, uh,

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nomenclature that's used. So, um, this is the two sinus B a v, um,

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that we just talked about. Um,

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also referred to as a SEAVERS type zero or you might hear biral

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non RA type. It's all the same thing. And then on the bottom,

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this is the one that's the fused. Um, so that's known as seavers type one.

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And you can see here we've got a right uh,

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leaflet and a left leaflet and then this big calcified ridge here.

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And the opening is just from here to here. This does not open it's fused.

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So this is again, the most common type. Um, and that's known as, um, uh,

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fused b a v, again, seavers type one, uh, or bi commissural, Rafa type.

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So these are,

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I put these in here just 'cause they're all different terms that you may see

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thrown around in the chart, for instance,

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for the patient and that sort of thing. So I just wanna make sure, you know, um,

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you're prepared to, to see all those different, different names and,

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and understand what they mean. Lastly,

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we're gonna go through some actual images themselves, but this is a, um,

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just some video clips of these two different versions.

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So on the left hand side we have the, the fused.

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So you can see that the right and left cusp are fused here.

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There's no opening between the two. This is the ra,

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not really thickened or calcified, maybe just a little bit of calcification. Um,

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but you can see that that fish mouth opening and then this is the two cusp kind,

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kind of the traditional only two cusp are visible. Um, more rare, um,

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but certainly we encounter it, uh, from time to time.

Report

Faculty

Stefan Loy Zimmerman, MD

Associate Professor of Radiology and Radiological Science

Johns Hopkins Medicine Department of Radiology and Radiological Science

Tags

Vascular

Idiopathic

Congenital

Cardiac valves

Cardiac

CTA

CT

Acquired/Developmental