Interactive Transcript
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It's going to case number seven case number
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seven is going to show some still images.
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I'm going to show some movies where it's probably good
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to look at the movies, right?
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Okay case number seven the history here
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is
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is a young woman who presents with?
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mono ocular blindness, I believe and
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and heart failure. So heart failure is
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a presentation a young woman who also has Oculus symptoms.
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This is a short axis view right ventricle left
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ventricle.
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I'm going to go show a long axis of your cine images
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show access then cine images in.
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Sorry, this is the delay enhancement that while it's there.
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Let's try to save there's any delay enhancement notice the bright areas in multiple
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multiple spots. Let's look at the fortune of
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you for chambercini image. That's a 4 chain
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basini image.
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And this young woman has heart failure.
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Now I'm going to put a still image of the delay enhancement and we'll keep
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this image on the screen while we answer
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the question young woman with heart failure.
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Delayed enhancement which image shown
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what is the correct answer multi-vessel coronary
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artery disease cardiac sarcoidosis erythogenic
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RV cardiomyopathy, idiopathic delicious cardiomyopathy or
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hypertrophic cardiomyopathy.
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If you can say unfortunately, neither of these of these
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are correct the correct diagnosis. He has cardiac sarcoidosis. This
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is a young woman who has
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dilated ventricles.
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Notes, I'm going to go back to the image findings noticeable the
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left and right ventricle. Sorry predomplay they
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left ventricle was dilated. It's moving poorly the
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ejection fractions under 35% and a key
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feature in this case was the pattern of delayed enhancement
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notice. There's multiple bright spots in
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the heart.
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Involving the sub endocardium, but also not involving the
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serbiancardium in some areas. For example here the not in
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a single coronary artery distribution, then multiple territories very unusual
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for a patient to get infarctions in multiple territories.
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And in areas which involve as well as do not
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involve the sub-indocardium.
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Furthermore. It's a younger patient ischemic heart
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disease unlike any younger patient though it can occur.
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The patient also has heart failure. So there's Global dysfunction
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some of disproportionate to
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the delay enhancement is also optic
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optic symptoms judge in this particular case due to
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opting neuropathy. So patient with cardiacodosis the key
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finding here is multiple areas of enhancement in non-ish
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gaming distribution in a younger patient
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non-ish gaming cardiomack, they consider
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cardiac sacredosis, which is under diagnosed in clinical practice or
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out in the clinical World particular and
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Mr. Is not shares the patient with cardiacredosis multiple
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patch areas of enhancement.
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And the patient who
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presented with heart failure and also has Oculus symptoms. Okay cardiacortes
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any questions as
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the there was some confusion now particularly with
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regard to the answers in this case, and it doesn't do not
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seem to be any credit any answers any any questions so far,
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so we'll go on to two more questions, but heading to this case
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Question number two asks, which are the
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following statement best characterizes cardiac sacredosis other
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majority of the patient's a symptomatic or asymptomatic is
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histological confirmation needed before treatment connection disturbances,
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maybe evident.
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consequent contraindicator of the pythonomic findings
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and agriculture so which is one of the best characterizes so
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there there's one statement here, which is
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correct. And the other statements can be considered incorrect or not.
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Not good choices. Okay. Can
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we take a poll of what audience thinks following best
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characterizes? Okay. Actually the correct answer here is
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C connection disturbances, maybe evident
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cardiac sarcoidosis typically presents with arithmias in
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conduction disturbances because it involves a basin septum heart
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block.
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Is a typical feature of cardiac syncretosis
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the others are wrong the majority
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of patients cardigosa asymptomatic.
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Histological confirmation is not needed before treatment because biopsy
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of the heart is very difficult. They're frauded
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complications and maybe falsely negative. So in histological
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confirmation, the heart is not needed before treatment started typical treatment
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is with conical steroids or with immunomodulators.
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They are not any pathogenic findings on Echo car
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geography While most abnormalities while thinning a wall
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thickening maybe seen But Echo is not is not
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Diagnostic in many case of cardiac sacredosis. And
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Connie Kamar is generally needed to
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evaluate for inflammation fibrosis. So
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cardiac sarcoidosis multi multiple areas of
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enhancement patchy enhancement typically involving the intervention.
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May present with typical presentations are arithmiers.
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conduction of normalities May proceed to have
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heart failure and sudden death
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typical treatments of Conquest steroids are immunomodulators particularly
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if there's active information, okay last question
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the commentary of scarring in cardiac sarcoders, which are
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the following segments basal interventric reception inferior left
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ventricle lateral left ventricle.
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and tree left ventrico or anterior right
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ventricle
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Typically, which areas affected by late Gallery
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enhancement oscarring and cardiacom and cardiac
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sarcoidosis is a question.
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Yeah basement of a nuclear symptom excellent a good choice the Communist
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area affected by by scarring or
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information contacts the basal interventricular septum as
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as demonstrated by his logical examination
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of Hearts. The other areas can be affected with
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the common areas the basal interventricular septum.
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So there's enhancement in Apache pattern the basil interventricular
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septum consider soccer doses.
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Codexancois has any questions on cardiac sarcoidosis lagenox
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any further questions and contactos. So I think
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we have time for
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for at least one more case. It's 10:53. I think
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we can proceed to case number eight.